Journal of Craniovertebral Junction and Spine

CASE REPORT
Year
: 2016  |  Volume : 7  |  Issue : 2  |  Page : 111--114

Cervicomedullary intramedullary peripheral primitive neuroectodermal tumor with intratumoral bleed: Report of one case and review of literature


Pradeep Sharma1, Kuntal K Das1, Anant Mehrotra1, Arun K Srivastava1, Rabi N Sahu1, Awadhesh Jaiswal1, Rakesh Pandey2, Sanjay Behari1, Kamlesh S Bhaisora1, Jayesh Sardhara1 
1 Department of Neurosurgery, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, Uttar Pradesh, India
2 Department of Pathology, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, Uttar Pradesh, India

Correspondence Address:
Kuntal K Das
Department of Neurosurgery, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow - 226 014 Uttar Pradesh
India

Primitive neuroectodermal tumors (PNET) are highly malignant, yet relatively uncommon neoplasms of the central nervous system. Although a host of different parts of the nervous system can be affected, intramedullary location of PNET is extremely rare. Most reports on intramedullary PNET have reported central PNET (cPNET); peripheral PNET (pPNET) affecting intramedullary spinal location is extremely rare. Till now, seven such cases of intramedullary pPNET have been described in medical literature in English. Here, we report an 11-year-old boy with cervicomedullary junction intramedullary pPNET who presented with intratumoral bleed, wherein the clinical presentation and radiological features gave us no clue preoperatively about the underlying diagnosis. In this report, we additionally review certain salient aspects of this dreaded disease in light of the existing evidence.


How to cite this article:
Sharma P, Das KK, Mehrotra A, Srivastava AK, Sahu RN, Jaiswal A, Pandey R, Behari S, Bhaisora KS, Sardhara J. Cervicomedullary intramedullary peripheral primitive neuroectodermal tumor with intratumoral bleed: Report of one case and review of literature.J Craniovert Jun Spine 2016;7:111-114


How to cite this URL:
Sharma P, Das KK, Mehrotra A, Srivastava AK, Sahu RN, Jaiswal A, Pandey R, Behari S, Bhaisora KS, Sardhara J. Cervicomedullary intramedullary peripheral primitive neuroectodermal tumor with intratumoral bleed: Report of one case and review of literature. J Craniovert Jun Spine [serial online] 2016 [cited 2021 Jan 25 ];7:111-114
Available from: https://www.jcvjs.com/article.asp?issn=0974-8237;year=2016;volume=7;issue=2;spage=111;epage=114;aulast=Sharma;type=0